Journal of Isfahan Dental School

Pulp Treatment Management of Primary Molars in Patient with Fanconi Anemia: A Case Report

Document Type : گزارش مورد

Authors

1 Associate Professor, Department of Pediatric Dentistry, School of Dentistry, Isfahan University of Medical Sciences, Isfahan, Iran

2 Postgraduate Student, Department of Pediatric Dentistry, School of Dentistry, Isfahan University of Medical Sciences, Isfahan, Iran

Abstract

Introduction: Fanconi anemia is a rare autosomal recessive disease that is associated with chromosome failure and impaired DNA repair. The aim of this study was to report a case of Fanconi anemia and to manage the treatment of deciduous tooth pulp and its periodic clinical follow-up.
Case Report: The patient is a six-year-old boy with a definitive diagnosis of Fanconi anemia who has referred to the Pediatric Dentistry Department of Isfahan University of Medical Sciences due to decayed deciduous teeth and pain. Some obvious signs such as short stature, hair, pigmented face, contiguous eyebrows, coarse hair, protruding forehead, flat nose bridge and large ears.
Conclusion: With despite the low platelet level, two teeth can be treated simultaneously in one session and no particular problem has been observed until the case is reported. It is recommended that taking into account the general health of the patient is very important in providing a treatment plan.
Key words: Fanconi anemia, Pediatric dentistry, Dental Pulp

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Journal of Isfahan Dental School
Volume 18, Issue 2 - Serial Number 2
June 2022
Pages 215-219